Oro-Dental Manifestations and Implications of the Osteolyses
Chetty, M1,3*, Roberts, T1,3, Stephen, L.X.G1,3, Bertie, J.D4, Beighton, P2,3
Affiliation
- 1Faculty of Dentistry, University of the Western Cape, Bellville, Cape Town, South Africa
- 2Division of Human Genetics, Faculty of Health Sciences, University of Cape Town, South Africa
- 3University of the Western Cape/ University of Cape Town Combined Dental Genetics Clinic, Red Cross Childrens Hospital, Cape Town, South Africa
- 4Department of Orthopaedics, Greys Hospital, Pietermaritzburg, South Africa
Corresponding Author
Professor Chetty, M., Faculty of Dentistry, University of the Western Cape/ University of Cape Town Combined Dental Genetics Clinic, Red Cross Childrens Hospital, Cape Town, South Africa, Tel: 021 9373112; E-mail: drmchetty@mweb.co.za
Citation
Chetty, M., et al. Oro-Dental Manifestations and Implications of the Osteolyses. (2017) J Dent Oral Care 3(2): 1- 5.
Copy rights
© 2017 Chetty, M. This is an Open access article distributed under the terms of Creative Commons Attribution 4.0 International License.
Keywords
Abstract
The Osteolyses are a group of uncommon genetic disorders which are characterized by progressive resorption of bone. This process ultimately results in significant physical handicap with pathological fractures representing an additional complication. The skeleton in the Osteolyses is radiolucent and the manifestations resemble those of Osteogenesis Imperfecta.
A boy with a confirmed diagnosis of Torg-Winchester syndrome attended the metabolic bone clinic at Grey’s Hospital and his clinical and radiological features have recently been published[1]. The dental and craniofacial manifestations of this boy form the subject of this article. These features tend to be overshadowed by the more dramatic skeletal changes in the limbs. Nevertheless, appropriate dental care is an important component of the overall management of this severe condition.
